CASE REPORT
Scleroderma-like syndrome in a patient with primary biliary cirrhosis
Online publication date: 2010-04-08
Reumatologia 2009;47(6):389-391
KEYWORDS
ABSTRACT
Primary biliary cirrhosis (PBC) is a chronic, progressive autoimmune disease of the liver marked by slow progressive destruction of the small interlobular bile ducts that leads to cholestasis, jaundice, liver cirrhosis and liver failure. Various skin manifestations have been described in patients with PBC including pruritus, skin excoriations, skin hyperpigmentation, scleroderma, morphea, lichen sclerosus et atrophicus, granuloma annulare, and atypical urticaria. In this paper we present a case of a 34-year old woman with PBC accompanied by scleroderma-like skin syndrome.
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Copyright: © Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie. This is an Open Access journal, all articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License (https://creativecommons.org/licenses/by-nc-sa/4.0/), allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license.
| eISSN: | 2084-9834 |
| ISSN: | 0034-6233 |
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