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OPIS PRZYPADKU
Samoograniczająca się młodzieńcza mucynoza skórna - opis przypadku.
 
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Data nadesłania: 22-11-2016
 
 
Data ostatniej rewizji: 30-01-2017
 
 
Data akceptacji: 15-02-2017
 
 
Data publikacji online: 22-03-2017
 
 
Data publikacji: 28-02-2017
 
 
Reumatologia 2017;55(1):61-64
 
SŁOWA KLUCZOWE
DZIEDZINY
STRESZCZENIE
Girl, aged 4 years old, began the disease with pain of the lower extremities, fever up to 38°C and signs of upper airway infection. Then the patient developed oedema and redness of the whole face, thickened skin, subcutaneous nodular foldings of the frontal, occipital, cervical and axillary regions, extensor areas of the joints; fine, hard whitish nodules in the frontal region and over interphalangeal joints of the hands, pruritus; oedemas of the ankles, knees and joints of the hands, cervical lymphadenopathy and hepatomegaly. Blood tests at the moment of the diagnosis revealed elevation of markers of inflammation as ESR and CRP, leukocytosis, thrombocytosis, hypoalbuminemia, and hyper-alfa-2-globulinemia. Histopathological examination of the skin biopsy specimen and subcutaneous tissue revealed myxoid subcutaneous tissue located under the dermis and a section consisting of myxoid mesenchymal tissue with inflammatory infiltration by histiocytic cells. The presence of acid mucopolysaccharides in fields of the myxoid tissue was also observed. The self-healing juvenile cutaneous mucinosis (SJCM) was diagnosed.
 
REFERENCJE (11)
1.
Montgomery H, Underwood LJ. Lichen myxedematosus; differentiation from cutaneous myxedemas or mucoid states.
 
2.
J Invest Dermatol 1953; 20: 213-236.
 
3.
Rongioletti F, Rebora A.Updated classification of popular mucinosis lichen myxedematosus, and scleromyxoedema. J Am Acad Dermatol 2001; 44: 273-281.
 
4.
Terlikowska-Brzósko A, Kwiek B, Glińska O. Dwa przypadki scleromyxedema. Przegl Dermatol 2010; 97: 378-385.
 
5.
Jenerowicz D, Ziembicka A, Piotrowska K. Lichen myxedematosus-diagnostic difficulties. A case report. Post Dermatol Alergol 2006; 23: 138-142.
 
6.
Colomb D, Racouchot J, Vittoni F. Mucinose d’evelution regressive sana paraproteine chez une jeune fille. Lyon Med 1973; 230; 474-475.
 
7.
Cowen EW, Scott GA, Mercurio MG. Self-healing juvenile cutaneous mucinosis. J Am Acad Dermatol 2004; 50: 97-100.
 
8.
Nagaraj LV, Fangman W, White WL. Self-healing juvenile cutaneous mucinosis: Cases highlighting subcutaneous/fascial involvement. J Am Acad Dermatol 2006; 55: 1036-1043.
 
9.
Pucevich MV, Latour DL, Bale GF. Self-healing juvenile cutaneous mucinosis. J Am Acad Dermatol 1984; 11: 327-332.
 
10.
Carder KR, Fitzpatrick JE, Weston WL, Morelli JG. Self-Healing Juvenile Cutaneous Mucinosis. Pediatric Dermatol 2003; 20: 35-39.
 
11.
Wadee S, Roode H, Schulz EJ. Self-healing juvenile cutaneous mucinosis in a patient with nephroblastoma. Clin Exp Dermatol 1994; 19: 90-93.
 
Copyright: © Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie. This is an Open Access journal, all articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License (https://creativecommons.org/licenses/by-nc-sa/4.0/), allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license.
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ISSN:0034-6233
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