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OPIS PRZYPADKU
Three atypical manifestations of granulomatosis with polyangiitis: lateral medullary syndrome, anterior cheek mass and melting scleritis of eye
 
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Data nadesłania: 24-11-2016
 
 
Data ostatniej rewizji: 31-01-2017
 
 
Data akceptacji: 21-05-2017
 
 
Data publikacji online: 18-07-2017
 
 
Data publikacji: 30-06-2017
 
 
Reumatologia 2017;55(3):145-150
 
SŁOWA KLUCZOWE
DZIEDZINY
STRESZCZENIE
Granulomatosis with polyangiitis (GPA, formerly Wegener granulomatosis) is a vasculitis with various organ involvement. There have been a few cases of CNS stroke and rare cases of lateral medullary infarction (LMI) as a manifestation of GPA. Also there have been reports of sinuses, nose and laryngeal masses mistakenly referred as carcinomas and subsequently GPA was diagnosed in their pathological reports. Another severe fulminant manifestation can be necrotizing scleritis leading to perforation of sclera. Therefore, here we present some rare and fulminant manifestations of GPA in 3 separate cases for further emphasis of the unusual manifestations of GPA that should always be kept in mind.
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ISSN:0034-6233
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