CASE REPORT
Eosinophilic fasciitis in a 5-year-old boy
Submission date: 2013-03-07
Acceptance date: 2013-03-28
Online publication date: 2013-06-26
Publication date: 2013-06-28
Reumatologia 2013;51(3):225-228
KEYWORDS
TOPICS
ABSTRACT
Eosinophilic fasciitis is a rare disease in childhood. We report the case of a 5-year-old boy who was admitted to our hospital with a 2-month history of generalised skin sclerosis, induration, erythema, peau d’orange,
groove sign, and painless joint contractures of multiple joints, which was preceded by a week of high fever. Laboratory tests revealed a peripheral eosinophilia. A full-thickness biopsy of skin-muscle and fascia confirmed the diagnosis of eosinophilic fasciitis. The patient received prednisolone, methotrexate, chloroquine, and
rehabilitation. Five months later the following were observed: better general health, reduction of skin and subcutaneous hardening,and better mobility of joints. In conclusion, eosinophilic fasciitis ought to be taken into differential diagnosis of generalised scleroderma with joint contractures in children. Combination therapy allows for improvement of efficiency.
groove sign, and painless joint contractures of multiple joints, which was preceded by a week of high fever. Laboratory tests revealed a peripheral eosinophilia. A full-thickness biopsy of skin-muscle and fascia confirmed the diagnosis of eosinophilic fasciitis. The patient received prednisolone, methotrexate, chloroquine, and
rehabilitation. Five months later the following were observed: better general health, reduction of skin and subcutaneous hardening,and better mobility of joints. In conclusion, eosinophilic fasciitis ought to be taken into differential diagnosis of generalised scleroderma with joint contractures in children. Combination therapy allows for improvement of efficiency.
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Copyright: © Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie. This is an Open Access journal, all articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License (https://creativecommons.org/licenses/by-nc-sa/4.0/), allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license.
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