CASE REPORT
Atypical course of Henoch-Schonlein purpura in an adult patient
More details
Hide details
Submission date: 2015-06-22
Final revision date: 2015-08-18
Acceptance date: 2015-08-20
Online publication date: 2015-09-21
Publication date: 2015-09-15
Reumatologia 2015;53(4):225-229
KEYWORDS
TOPICS
ABSTRACT
Henoch-Schonlein purpura is vasculitis of small blood vessels characterized by deposits of IgA immune complexes and also non-thrombocytopenic purpura, abdominal pain, arthritis and renal involvement. It affects people of all ages, but most cases occur in children between 2 and 11 years old, more frequently in boys. The disease is much less common in adults, who often have a more severe course of the disease. The paper presents the case of a 38-year-old female patient with insidious course of the disease, initially dominant skin symptoms and joint pain without signs of inflammation. Symptoms of the disease were initially uncharacteristic and mild, and did not suggest severe and rapid course of the disease. The patient required hospitalization in several departments before final diagnosis of Henoch-Schonlein purpura. The patient was treated with corticosteroids and immunosuppression. Despite the rapid course of the disease, treatment was effective. The patient was discharged in good condition.
REFERENCES (18)
1.
Małecki R, Staworska K, Frankowski M, et al. Plamica Schönleina-Henocha o ciężkim przebiegu z zajęciem przewodu pokarmowego. Reumatologia 2012; 50: 61-65.
2.
Wardyn K, Życińska K, Życiński K. Plamica Schönleina-Henocha. Pierwotne układowe zapalenie naczyń. Wydawnictwo Medyczne Urban & Partner, Wrocław 2004; 284-288.
3.
Bujakowska O, Saracyn M, Kur-Zalewska J, et al. Dramatyczny przypadek plamicy Schönleina-Henocha u osoby dorosłej. Reumatologia 2013; 51: 229-232.
4.
Fauci A, Pazdur J. Plamica Schönleina-Henocha. Harrison – Reumatologia. Wyd. II. Wydawnictwo Czelej, Lublin 2012; 188-189.
5.
Pillebout E, Thervet E, Hill G. Henoch-Schonlein purpura in adults: outcome and prognostic factors. J Am Soc Nephrol 2002; 13; 1271-1278.
6.
Małdyk H, Fiedorowicz-Fabrycy I. Układowe zapalenie naczyń. Reumatologia 2004; 42 (supl. 1): 86-87.
7.
Romicka A, Rostropowicz-Denisiewicz K. Plamica Schonleina-Henocha. Zarys reumatologii wieku rozwojowego. Wydawnictwo Elamed, Katowice 2010; 133-135.
8.
Zapalenie naczyń związane z IgA. Interna Szczeklika. Medycyna Praktyczna, Kraków 2014; 1889-1890.
9.
Jaliman D. Henoch-Schonlein Purpura. July 12, 2013. 2013 WebMD.
10.
Maj J, Reich A, Baran E. Pierwotne systemowe zapalenie naczyń. PSV. Postępy Dermatologii i Alergologii 2004; 21: 247-254.
11.
Jennette JC, Falk RJ, Bacon PA, et al. 2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides. Arthritis Rheum 2013; 65: 1-11.
12.
Brogan P, Elefherion D, Dillon M. Small vessel vasculitis. Pediatr Nephrol 2010; 25: 1025-1035.
13.
Zaffarello M, Fanos V. Treatment-based literature of Henoch-Schonlein purpura nephritis in childhood. Pediatr Nephrol 2009; 24: 1901-1911.
14.
Frigui M, Lehiani D, Konbae M. Acute pancreatic as initial manifestation of adult Henoch-Schonlein purpura: raport of case and review of literature. Eur J Gastroenteral Hepatol 2011; 23: 189-192.
15.
Zimmermann-Górska I. Plamica Henocha-Schönleina. Reumatologia kliniczna. Wydawnictwo Lekarskie PZWL, Warszawa 2008; 1019-1020.
16.
Rieu P, Noel H. Henoch-Schonlein nephritis in children and adults, morphological features and clinicopathological correlations. Ann Med Interna 1999; 150: 151-159.
17.
López Meiller MJ, Cavallasca JA, Maliandi Mdel R, Nasswetter GG. Henoch-Schonlein purpura in adults. Clinics 2008; 63: 273-276.
18.
Wiland P, Madej M. Zapalenie naczyń. Przegląd Reumatologiczny 2007; 3-5.
Copyright: © Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie. This is an Open Access journal, all articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License (
https://creativecommons.org/licenses/by-nc-sa/4.0/), allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license.