CASE REPORT
Benign joint hypermobility syndrome
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Submission date: 2014-10-21
Final revision date: 2014-11-12
Acceptance date: 2014-11-13
Online publication date: 2014-11-30
Publication date: 2014-12-31
Reumatologia 2014;52(6):398-401
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ABSTRACT
Benign joint hypermobility syndrome (BJHS), commonly known as loose ligament syndrome, is a non-inflammatory rheumatic condition. It is characterised by a greater than normal range of motion of the joints of the limbs and spine. The prevalence of the syndrome in preschool-age children is estimated to be between 2% and 30%, depending on ethnic background (with higher prevalence in Asian and African populations), occurring most often in families with a history of the condition and more frequently in girls. This paper presents a case report of a 12-year-old girl. A broad differential diagnostic approach to recurrent joint inflammation with joint effusion and pain made it possible to establish a diagnosis of benign joint hypermobility syndrome. The child met the Brighton criteria; her Beighton score was 7 out of 9. Patient education aimed at eliminating abnormal joint movement and an appropriate rehabilitation programme play key roles in the treatment of BJHS.
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