Retroperitoneal fibrosis – a review of the literature and own experience

Retroperitoneal fibrosis (RPF) is a rare disease of unclear pathogenesis. It is characterized by the presence of a fibro-inflammatory mass usually surrounding the abdominal aorta and the iliac arteries. Early diagnosis and appropriate treatment is crucial in order to avoid severe complications. This review summarizes the actual knowledge on RPF. We also propose a treatment algorithm based on the available literature and our own experience.

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